Abstract. Background: Hypertrophic pachymeningitis is an uncommon disorder that causes a localized or diffuse thickening of the dura mater and has been. Summary: Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is. Hypertrophic pachymeningitis is a unique clinical entity characterised by fibrosis and thickening of the duramater with resulting neurological dysfunction.

Author: Dogar Zugore
Country: Uzbekistan
Language: English (Spanish)
Genre: Education
Published (Last): 16 February 2012
Pages: 132
PDF File Size: 5.42 Mb
ePub File Size: 19.6 Mb
ISBN: 374-4-80639-477-8
Downloads: 73741
Price: Free* [*Free Regsitration Required]
Uploader: Tygosho

Hypertrophic pachymeningitis | Radiology Reference Article |

Both the patient’s routine biochemistry was pacgymeningitis, and they were further evaluated to rule out secondary causes The serum was negative for rheumatoid factor, antinuclear antibodies. Pacjymeningitis succesful case of hypertrophic cranial pachymeningitis treated with optic nerve decompression. Multiple meningiomas Multiple meningiomas. J Neurol Sci ; Can J Neurol Sci ; P-ANCA positive Wegener’s granulomatosis presenting with hypertrophic pachymeningitis and multiple cranial neuropathies: Open access journal indexed with Index Medicus.

Support Radiopaedia and see fewer ads.

A study of seven cases. Author information Article notes Copyright and License information Disclaimer.

Hypertrophic pachymeningitis

Cerebrospinal fluid analysis revealed normal cell count, protein and sugar levels. There was bilateral involvement of trochlear nerve and partial involvement of oculomotor nerve on the left side.


Uncommon findings in idiopathic hypertrophic cranial pachymeningitis. Neurological examination showed right hemiparesis, which recovered in 2 days. A year-old lady presented with headache and progressive painless loss of vision in both the eyes over a periods of 6 months.

Hypertropihc pachymeningitis of unknown origin: Case 1 Case 1. Arch Neurol Psychiatry; This report describes two cases of hypertrophic cranial pachymeningitis and briefly discusses the clinical and radiographic, findings.

Clinicoradiological spectrum and therapeutic options.

Idiopathic hypertrophic pachymeningitis.

Neurol Med Chir ; J Neurol Neurosurg Psychiatry ; Idiopathic hypertrophic pachymeningeal lesions: Introduction Hypertrophic pachymeningitis is a rare form of diffuse inflammatory disease that causes thickening of the dura mater.

Combined therapy of corticosteroid and azathioprine in hypertrophic cranial pachymeningitis. National Center pachymeningiyis Biotechnology InformationU.

Surg Neurol ; Hypertrophic cranial pachymeningitis involving dural sinuses: CT or MR imaging studies should be obtained to identify mass lesions in the brain stem or skull base. Case 2 Case 2. Idiopathic hypertrophic pachymeningitis is a rare disorder of unknown origin. Axial section of MRI image showing diffuse enhacement with thickening of meninges. Cases and figures Imaging differential diagnosis. Magnetic resonance imaging MRI of the brain showed diffuse enhancement with thickening of the meninges.


Exact etiopathogenesis of this entity is still unknown, but it is speculated to be an autoimmune phenomenon or occur as a direct result of infectious or infiltrative pathology. Case Reports Case 1 A year-old lady presented with headache and progressive painless loss of vision in both the eyes over a periods of 6 months. Thank you for updating your details.

Ann Indian Acad Neurol. Idiopathic hypertrophic cranial pachymeningitis hypertrophci perifocal brain edema.

Rest of the neurological examination was normal. MR imaging of the meninges.

Hypertrophic pachymeningitis

Please review our privacy policy. Recurrent cranial neuropathy as a clinical presentation of idiopathic inflammation of the duramater: Neuropathological findings of six cases including two autopsied cases are also presented.

There were no giant cells, caseation necrosis, or epitheloid granuloma.